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Tricuspid atresia

**{{{Name|Tricuspid atresia}}}**
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ICD-10	{{ICD10
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 ICD9           = 746.1|
 ICDO           = |
 Image          = |
 Caption        = |
 OMIM           = 605067 |
 MedlinePlus    = 001110 |
 eMedicineSubj  = med |
 eMedicineTopic = 2313 |
 DiseasesDB     = |

}} Tricuspid atresia is a form of congenital heart diseasewhereby there is a complete absence of the tricuspid valve. Therefore, there is an absence of right atrioventricular connection. This leads to a hypoplastic or an absence of the right ventricle.

Because of the lack of an A-V connection, an atrial septal defect(ASD) must be present to maintain blood flow. Also, since there is a lack of a right ventricle there must be a way to pump blood into the pulmonary arteries, and this is accomplished by a ventricular septal defect(VSD).

Blood is mixed in the left atrium. Because the only way the pulmonary circulation receives blood is through the VSD, a patent ductus arteriosusis usually also formed to increase pulmonary flow.

Clinical manifestations

progressive cyanosis
poor feeding
tachypneaover the first 2 weeks of life
holosystolicmurmurdue to the VSD
superior axisand left ventricular hypertrophy(since it must pump blood to both the pulmonary and systemic systems)
normal heart size

Treatment

PGE1to maintain patent ductus arteriosus
modified Blalock-Taussigshunt to maintain pulmonary blood flow by placing a Gortex conduitbetween the subclavian arteryand the pulmonary artery.
cavopulmonary anastomosis (hemi-Fontanor bidirectional Glenn) to provide stable pulmonary flow
Fontan procedureto redirect inferior vena cavaand hepatic veinflow into the pulmonary circulation

External links

Tricuspid Atresia informationfrom Seattle Children's Hospital Heart Center

This article is licensed under the GNU Free Documentation License.
It uses material from the http://en.wikipedia.org/wiki/Tricuspid+atresia Wikipedia article Tricuspid atresia.

All text is available under the terms of the GNU Free Documentation License